p-ISSN: 1306-696x | e-ISSN: 1307-7945
Turkish Journal of Trauma and Emergency Surgery
PEUTZ JEGHERS SYNDROME [Ulus Travma Acil Cerrahi Derg]
Ulus Travma Acil Cerrahi Derg. 1999; 5(2): 132-133
PEUTZ JEGHERS SYNDROME
Ahmet Yılmaz1, Kadri Güler1, Hakan Bozkurtoğlu1, Faik Çelik1SSK Göztepe Eğitim Hastanesi 4. Cerrahi Kliniği
Peutz - Jeghers Syndrome is a rare, inherited autozomal dominant disease characterized by gastrointestinal hamartomatous polyps and mucocutaneous pigmentation. In this paper we report two cases of Peutz -Jeghers syndrome who were admitted and operated with intussusception. Screening their family members revealed intestinal and extraintestinal manifestations of the disease and no malignancy was detected.
Keywords: PEUTZ-JEGHERS SYNDROME, INTUSSUSCEPTION
PEUTZ JEGHERS SENDROMU
Ahmet Yılmaz1, Kadri Güler1, Hakan Bozkurtoğlu1, Faik Çelik1SSK Göztepe Eğitim Hastanesi 4. Cerrahi Kliniği
Ahmet Yılmaz, Kadri Güler, Hakan Bozkurtoğlu, Faik Çelik. PEUTZ JEGHERS SYNDROME. Ulus Travma Acil Cerrahi Derg. 1999; 5(2): 132-133